Organic Acids

Source	Urine
Mnemonic	BGLNON BGL Non-Blood Test Name Prompt: Organic Acids
Specimen Requirements	Prefer at least 10 mL random urine, first morning void if possible (at least 5 mL for infants).
Specimen Handling	If specmien is transferred to a secondary container, indicate specimen type on label. PSC: Send on ice to DSC. RRL: Send on ice to ACH. Extra-regional: Freeze immediately and maintain frozen during transport to DSC.
Additional Information	Send a copy of the requisition with the specimen. Metabolites reported (truncated list): lactic acid, glycolic acid, oxalic acid, 2-oxovaleric acid, methylmalonic acid, methylmalonic 4-hydroxybutyric acid, 2-oxo-3-methylvaleric acid, ethylmalonic acid, 2-oxoisocaproic acid, furamic acid, glutaric acid, 3-methylglutaric acid, succinylacetone, adipic acid, pyroglutamic acid, oxoproline, 2-hydroxyglutaric acid, 3-hydroxy-3-methylglutaric acid, suberic acid, sebacic acid, 3-hydroxypropionic acid, 3-hydroxyisovaleric acid, isovalerylglycine, glyceric acid, propionylglycine, tiglylglycine, 3-hydroxyglutaric acid, methylcitric acid, homogentisic acid, phenylpropionylglycine, suberylglycine.
Testing Location	ACH Biochemical Genetics Lab
Testing Frequency	Weekly; must notify ACH Biochemical Genetics Lab for stat turn-around.
Alternate Name(s)
Reference Interval	Provided on test report